p38 Mitogen-Activated Protein Kinase- and HuR-Dependent Stabilization of p21Cip1 mRNA Mediates the G1/S Checkpoint V Lafarga, A Cuadrado, I Lopez de Silanes, R Bengoechea, ... Molecular and cellular biology 29 (16), 4341-4351, 2009 | 294 | 2009 |
Prion-like nuclear aggregation of TDP-43 during heat shock is regulated by HSP40/70 chaperones M Udan-Johns, R Bengoechea, S Bell, J Shao, MI Diamond, HL True, ... Human molecular genetics 23 (1), 157-170, 2014 | 139 | 2014 |
TDP-43 localizes in mRNA transcription and processing sites in mammalian neurons I Casafont, R Bengoechea, O Tapia, MT Berciano, M Lafarga Journal of structural biology 167 (3), 235-241, 2009 | 103 | 2009 |
Cajal’s contribution to the knowledge of the neuronal cell nucleus M Lafarga, I Casafont, R Bengoechea, O Tapia, MT Berciano Chromosoma 118, 437-443, 2009 | 74 | 2009 |
Myopathy associated BAG3 mutations lead to protein aggregation by stalling Hsp70 networks M Meister-Broekema, R Freilich, C Jagadeesan, JN Rauch, ... Nature communications 9 (1), 5342, 2018 | 69 | 2018 |
Reorganization of Cajal bodies and nucleolar targeting of coilin in motor neurons of type I spinal muscular atrophy O Tapia, R Bengoechea, A Palanca, R Arteaga, JF Val-Bernal, ... Histochemistry and cell biology 137, 657-667, 2012 | 63 | 2012 |
Cajal body number and nucleolar size correlate with the cell body mass in human sensory ganglia neurons MT Berciano, M Novell, NT Villagra, I Casafont, R Bengoechea, ... Journal of structural biology 158 (3), 410-420, 2007 | 62 | 2007 |
Myopathy-causing mutations in an HSP40 chaperone disrupt processing of specific client conformers KC Stein, R Bengoechea, MB Harms, CC Weihl, HL True Journal of Biological Chemistry 289 (30), 21120-21130, 2014 | 60 | 2014 |
SUMO-1 transiently localizes to Cajal bodies in mammalian neurons J Navascues, R Bengoechea, O Tapia, I Casafont, MT Berciano, ... Journal of structural biology 163 (2), 137-146, 2008 | 51 | 2008 |
Hsp70 chaperones and type I PRMTs are sequestered at intranuclear inclusions caused by polyalanine expansions in PABPN1 JP Tavanez, R Bengoechea, MT Berciano, M Lafarga, M Carmo-Fonseca, ... PloS one 4 (7), e6418, 2009 | 50 | 2009 |
The giant fibrillar center: a nucleolar structure enriched in upstream binding factor (UBF) that appears in transcriptionally more active sensory ganglia neurons I Casafont, R Bengoechea, J Navascués, E Pena, MT Berciano, ... Journal of structural biology 159 (3), 451-461, 2007 | 43 | 2007 |
Myofibrillar disruption and RNA-binding protein aggregation in a mouse model of limb-girdle muscular dystrophy 1D R Bengoechea, SK Pittman, EP Tuck, HL True, CC Weihl Human molecular genetics 24 (23), 6588-6602, 2015 | 42 | 2015 |
Nucleolar targeting of coilin is regulated by its hypomethylation state O Tapia, R Bengoechea, MT Berciano, M Lafarga Chromosoma 119, 527-540, 2010 | 35 | 2010 |
Mutations in the J domain of DNAJB6 cause dominant distal myopathy J Palmio, PH Jonson, M Inoue, J Sarparanta, R Bengoechea, M Savarese, ... Neuromuscular Disorders 30 (1), 38-46, 2020 | 30 | 2020 |
Nuclear speckles are involved in nuclear aggregation of PABPN1 and in the pathophysiology of oculopharyngeal muscular dystrophy R Bengoechea, O Tapia, I Casafont, J Berciano, M Lafarga, MT Berciano Neurobiology of disease 46 (1), 118-129, 2012 | 30 | 2012 |
The SMN Tudor SIM-like domain is key to SmD1 and coilin interactions and to Cajal body biogenesis O Tapia, V Lafarga, R Bengoechea, A Palanca, M Lafarga, MT Berciano Journal of cell science 127 (5), 939-946, 2014 | 29 | 2014 |
Nuclear compartmentalization and dynamics of the poly (A)-binding protein nuclear 1 (PABPN1) inclusions in supraoptic neurons under physiological and osmotic stress conditions NT Villagra, R Bengoechea, JP Vaqué, J Llorca, MT Berciano, M Lafarga Molecular and Cellular Neuroscience 37 (3), 622-633, 2008 | 29 | 2008 |
Inhibition of DNAJ-HSP70 interaction improves strength in muscular dystrophy R Bengoechea, AR Findlay, AK Bhadra, H Shao, KC Stein, SK Pittman, ... The Journal of clinical investigation 130 (8), 4470-4485, 2020 | 27 | 2020 |
Lithium chloride corrects weakness and myopathology in a preclinical model of LGMD1D AR Findlay, R Bengoechea, SK Pittman, TF Chou, HL True, CC Weihl Neurology: Genetics 5 (2), e318, 2019 | 25 | 2019 |
Characterization of a new SUMO-1 nuclear body (SNB) enriched in pCREB, CBP, c-Jun in neuron-like UR61 cells J Navascués, R Bengoechea, O Tapia, JP Vaqué, M Lafarga, ... Chromosoma 116, 441-451, 2007 | 23 | 2007 |